English



■Detailed data
Sex female
Age 00-04
Misc 1985-1989
Chief Complaint Fever、pancytopenia
Past history Carbamyl phosphate synthetase Ⅰdeficiency (CPSD)in 3 months was diagnosed.
Present history And hospitalized for hepatomegaly, leukopenia was observed abnormal liver function is pointed out where they visited a nearby physician fever loss of appetite was observed (40 ℃) is persistent. Hepatosplenomegaly, abnormal liver function, pancytopenia, and hospital admission for the purpose of scrutiny for a case report coagulation abnormalities (38- 39 ℃) is persistent fever after hospitalization. Axillary lymph node swelling, neck (+), hepatosplenomegaly (+), mild jaundice skin (+)
Laboratory findings WBC1.6×10³/μl、RBC2.62×106/μl、Hb 6.9g/dl、Ht21.5%、MCV82.1fl、PLT5.4×104/μl、BM-NCC8.1×104/μl、LDH84,100U/l、AST11,010U/l、ALT24,700U/l、Fbg68mg/dl以下、FDP15.3μg/ml、T-bil.13.6mg/dl、D-bil.12.7mg/dl、AST432U/l、ALT93U/l、LDH3,822U/l、
Ferritin14,105ng/ml、CRP0.2mg/dl、EB-VCAIgGx160(+)、EBNA-IgG(-)