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■Detailed data
Sex male
Age 00-04
Misc 1995-1999
Type of cases Rare
Chief Complaint Pancytopenia
Past history Atopic dermatitis(eight months)
Present history Admitted to our hospital and our department hepatosplenomegaly is increased to eight months a year old, is pointed pancytopenia. Although there is no bleeding spots, eczema may amount, around through both ears, the neck, swollen lymph nodes in the groin admit the left side of the neck and both. Hepatomegaly is about 12cm, the blunt edge is right subcostal, palpable about 15cm below the left hypochondrium. No abnormal facial appearance.
Laboratory findings WBC3.1×10³/μl、RBC3.45×106/μl、Hb8.0g/dl、Ht25.4%、MCV73.7fl、PLT5.3×104/μl、BM-NCC8×104/μl、LDH833U/l、Fe54μg/dl、UIBC428μg/dl
【additional test】Acid phospahatase、Angiotensin-coverting enzyme
Amino acid analysis・Organic analysis:not particular