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■Detailed data
FAB Group > Others
Sex female
Age 00-04
Misc 1990-1994
Chief Complaint 【At the initial diagnosis】
Easy infectious and granulocytopenia.
Past history 【2 years before the first visit】
Kostoman's syndrome
Present history 【Two year before the initial visit】
A Caesarean delivery was performed due to imminent fetal asphyxia. The gestational age was 38 weeks, and the birth weight was 2,686g. Poor sucking was observed after three days of life with the onset of a fever, redness around the anus,and splenohepatomegaly.
The neutrophil count was 7% (837.2/μl) of. Leukocytosis (11,960/μl). Pseudomonous aeruginosa was detected at the inflammation sites around the anus. The patient improved following the administration of antibiotics. The inflammation of the skin and fever recurred and the patient was transferred to this hospital at the age of two months.
【Present illness on admission】Her general status was good, BT 36.8℃, no Anemia, liver 3 cm, spleen 1 cm, and puriform eruptions in the ambilateral postauricular regions.
Laboratory findings 【The initial finding data】
WBC 7.5×10³/μl(Seg1.0, Ly76.5, Mo17.0 Eo5.0, At.ly0.5%)、RBC 3.81×106/μl、
Hb 9.9g/dl、Ht 32.9%、MCV 86.3fl、MCH 26.0pg、MCHC 30.1%、PLT 61.8×104/μl、
NCC 23.8×104/μl、Mgk 68/μl、
LD 483IU/l、TP 5.4g/dl、CRP 1.6mg/dl、
BUN 7.0mg/dl、UA 8.4mg/dl、AST 18IU/l、
IgG 610mg/dl(κ-type)、IgA 40mg/dl、IgM 124mg/dl
【One year after hospitalization】
WBC 9.2×10³/μl (Seg0.0, Ly40.0, Mo55.0, Eo1.0, Ba2.0, At.ly2.0%)、RBC 1.81×106/μl、Hb 5.9g/dl、Ht 16.3%、MCV 90.0fl、MCH 32.5pg、MCHC 27.6%、PLT 2.6×104/μl、
NCC 13.6×104/μl、Mgk 31.0/μl